The University of Chicago Header Logo

Connection

James A. Mastrianni to Prions

This is a "connection" page, showing publications James A. Mastrianni has written about Prions.
Connection Strength

3.102
  1. Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease. J Neurosci. 2012 Sep 05; 32(36):12396-405.
    View in: PubMed
    Score: 0.414
  2. The prion diseases. J Geriatr Psychiatry Neurol. 2010 Dec; 23(4):277-98.
    View in: PubMed
    Score: 0.363
  3. A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. J Neurosci. 2009 Aug 12; 29(32):10072-80.
    View in: PubMed
    Score: 0.335
  4. Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation. J Virol. 2007 Mar; 81(6):2831-7.
    View in: PubMed
    Score: 0.279
  5. Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia. Ann Neurol. 2005 Dec; 58(6):858-64.
    View in: PubMed
    Score: 0.259
  6. The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation. J Biol Chem. 2005 Jul 22; 280(29):27236-43.
    View in: PubMed
    Score: 0.250
  7. Wrinkles and folds of the prion protein. Neurology. 2003 Nov 11; 61(9):1168-9.
    View in: PubMed
    Score: 0.225
  8. Anle138b prevents PrP plaque accumulation in Tg(PrP-A116V) mice but does not mitigate clinical disease. J Gen Virol. 2019 06; 100(6):1027-1037.
    View in: PubMed
    Score: 0.164
  9. Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease. Neurology. 1996 Nov; 47(5):1305-12.
    View in: PubMed
    Score: 0.138
  10. Familial prion disease with Alzheimer disease-like tau pathology and clinical phenotype. Ann Neurol. 2011 Apr; 69(4):712-20.
    View in: PubMed
    Score: 0.094
  11. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Ann Neurol. 2010 Aug; 68(2):162-72.
    View in: PubMed
    Score: 0.090
  12. A novel human disease with abnormal prion protein sensitive to protease. Ann Neurol. 2008 Jun; 63(6):697-708.
    View in: PubMed
    Score: 0.077
  13. The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPSc. J Virol. 2006 Sep; 80(17):8521-9.
    View in: PubMed
    Score: 0.068
  14. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A. 2003 Apr 15; 100(8):4784-9.
    View in: PubMed
    Score: 0.054
  15. Inherited prion disease caused by the V210I mutation: transmission to transgenic mice. Neurology. 2001 Dec 26; 57(12):2198-205.
    View in: PubMed
    Score: 0.049
  16. The prion diseases. Semin Neurol. 2000; 20(3):337-52.
    View in: PubMed
    Score: 0.043
  17. Prion protein conformation in a patient with sporadic fatal insomnia. N Engl J Med. 1999 May 27; 340(21):1630-8.
    View in: PubMed
    Score: 0.041
  18. A transmembrane form of the prion protein in neurodegenerative disease. Science. 1998 Feb 06; 279(5352):827-34.
    View in: PubMed
    Score: 0.038
  19. The prion diseases: Creutzfeldt-Jakob, Gerstmann-Sträussler-Scheinker, and related disorders. J Geriatr Psychiatry Neurol. 1998; 11(2):78-97.
    View in: PubMed
    Score: 0.037
  20. Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein. Cell. 1995 Oct 06; 83(1):79-90.
    View in: PubMed
    Score: 0.032
  21. Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene. Mol Med. 1995 Sep; 1(6):607-13.
    View in: PubMed
    Score: 0.032
  22. Identifying key components of the PrPC-PrPSc replicative interface. J Biol Chem. 2008 Dec 05; 283(49):34021-8.
    View in: PubMed
    Score: 0.020
Connection Strength

The connection strength for concepts is the sum of the scores for each matching publication.

Publication scores are based on many factors, including how long ago they were written and whether the person is a first or senior author.