10713113Volchenboum SL, Vockley JThe Journal of biological chemistryAmino Acid Metabolism, Inborn Errors; Mitochondria; Mutation; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Protein Processing, Post-TranslationalAcyl Coenzyme A; Amino Acid Sequence; Biological Transport; Enzyme Stability; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Models, Molecular; Molecular Sequence Data; Open Reading Frames; Pentanoic Acids; Protein Conformation; Sequence Homology, Amino AcidMitochondrial import and processing of wild type and type III mutant isovaleryl-CoA dehydrogenase. J Biol Chem. 2000 Mar 17; 275(11):7958-63.J Biol Chem2000-03-17T00:00:002000Mitochondrial import and processing of wild type and type III mutant isovaleryl-CoA dehydrogenase.plugins:FeaturedVideosFeatured Videosplugins:TwitterTwitterprns:emailEncryptedemail addressprns:fullNamefull nameprns:hasAuthorListauthor listprns:hasNetworkhas networkprns:hasPublicationVenuepublished inprns:hasSubjectAreaMajorTopicListhas major subject area listprns:hasSubjectAreaMinorTopicListhas minor subject area listprns:informationResourceReferenceinformation resource referenceprns:isPrimaryPositionis primary positionprns:latitudelatitudeprns:longitudelongitudeprns:mainImagephotoprns:maxWeightmaximum weightprns:medlineTAjournal title abbreviationprns:meshDescriptorUIMeSH DescriptorUIprns:meshSemanticGroupNameMeSH semantic group nameprns:minWeightminimum weightprns:numberOfAuthorsnumber of authorsprns:numberOfConnectionsnumber of connectionsprns:numberOfPublicationsnumber of publicationsprns:personIdPerson IDprns:personInPrimaryPositionperson in primary positionprns:pluginSearchableDataProfilesRNS Plugin Searchable Dataprns:positionInDepartmentposition in departmentprns:predicateNodepredicate nodeprns:publicationDatepublication dateprns:sortOrdersort orderprns:uniquenessWeightuniqueness weightprns:yearyearAcademic ArticleArticleDocumentbibo:pmidPubMed Identifiervivo:authorRankauthor rank in publicationAuthorshipDepartmentvivo:hasSubjectAreahas subject areavivo:hrJobTitleHR job titleInformation Resourcevivo:informationResourceInAuthorshipauthorsvivo:linkAnchorTextlink anchor textvivo:linkedAuthorlinked authorvivo:linkedInformationResourcelinked information resourcePositionvivo:positionInOrganizationposition in organizationvivo:preferredTitlepreferred titleURLLinkvivo:webpagewebpagerdf:predicatepredicaterdf:typetyperdfs:labellabelConceptAgentfoaf:firstNamefirst namefoaf:lastNamelast nameOrganizationPersonD000214Chemicals & Drugs11170.993707Acyl Coenzyme AD000592Disorders8110.995804Amino Acid Metabolism, Inborn ErrorsD000595Genes & Molecular Sequences43920620.736832Amino Acid SequenceD001692Physiology1613960.915086Biological TransportD007930Chemicals & Drugs45670.984219LeucineD008958Concepts & Ideas24512840.706981Models, MolecularAuthorship 171281D008969Concepts & IdeasGenes & Molecular Sequences56030290.690359Molecular Sequence DataD009154Physiology70239520.442682MutationD010088Chemicals & Drugs531110.953147OxidoreductasesD011487Concepts & Ideas1998810.794238Protein ConformationD011499Physiology1523710.819179Protein Processing, Post-TranslationalD006801Living Beings2262862810.130064HumansD017386Concepts & IdeasGenes & Molecular Sequences1834160.921866Sequence Homology, Amino Acid0.1890340.1890341authors10.2520has subject areaPediatrics-Hematology and OncologyD008928AnatomyPhysiology2095350.748762MitochondriaD016366Genes & Molecular Sequences761170.958769Open Reading FramesD045782Chemicals & Drugs560.99761HemiterpenesD044925Chemicals & Drugs690.992438Oxidoreductases Acting on CH-CH Group DonorsD050769Chemicals & Drugs130.99945Isovaleryl-CoA Dehydrogenasehttp://www.uchospitals.edu/physicians/samuel-volchenboum.htmlClinical Pagehttps://voices.uchicago.edu/volchenboum/Sam Volchenboumhttps://ome.bsd.uchicago.eduOffice of Master's Educationhttp://commons.cri.uchicago.eduPediatric Cancer Data CommonsSamVolchenboumD004795Concepts & Ideas32390.991711Enzyme StabilityD010421Chemicals & Drugs660.996601Pentanoic AcidsUniversity of ChicagoSamuel L.VolchenboumxG5/K7QWEeXakH1rLkPq5g==Samuel L. Volchenboum41.78927490000000-87.6012500000000063Volchenboum, Samuel L.Professortrue1ProfessorProfessor