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Raymond P. Roos to Amyotrophic Lateral Sclerosis

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This is a "connection" page, showing publications Raymond P. Roos has written about Amyotrophic Lateral Sclerosis.
Raymond P. Roos
Connection Strength
8.796
Amyotrophic Lateral Sclerosis
  1. Machine learning predicts translation initiation sites in neurologic diseases with nucleotide repeat expansions. PLoS One. 2022; 17(6):e0256411.
    View in: PubMed
    Score: 0.760
  2. Knockdown of GADD34 in neonatal mutant SOD1 mice ameliorates ALS. Neurobiol Dis. 2020 03; 136:104702.
    View in: PubMed
    Score: 0.641
  3. Single chain variable fragment antibodies directed against SOD1 ameliorate disease in mutant SOD1 transgenic mice. Neurobiol Dis. 2019 01; 121:131-137.
    View in: PubMed
    Score: 0.586
  4. Venous thromboembolism after diaphragm pacing in amyotrophic lateral sclerosis. Muscle Nerve. 2014 Nov; 50(5):863-5.
    View in: PubMed
    Score: 0.446
  5. Guanabenz, which enhances the unfolded protein response, ameliorates mutant SOD1-induced amyotrophic lateral sclerosis. Neurobiol Dis. 2014 Nov; 71:317-24.
    View in: PubMed
    Score: 0.443
  6. An enhanced integrated stress response ameliorates mutant SOD1-induced ALS. Hum Mol Genet. 2014 May 15; 23(10):2629-38.
    View in: PubMed
    Score: 0.423
  7. Single chain variable fragment antibodies block aggregation and toxicity induced by familial ALS-linked mutant forms of SOD1. Neurobiol Dis. 2013 Aug; 56:74-8.
    View in: PubMed
    Score: 0.404
  8. Selective knockdown of mutant SOD1 in Schwann cells ameliorates disease in G85R mutant SOD1 transgenic mice. Neurobiol Dis. 2012 Oct; 48(1):52-7.
    View in: PubMed
    Score: 0.380
  9. The unfolded protein response in familial amyotrophic lateral sclerosis. Hum Mol Genet. 2011 Mar 01; 20(5):1008-15.
    View in: PubMed
    Score: 0.343
  10. Mutant SOD1 knockdown in all cell types ameliorates disease in G85R SOD1 mice with a limited additional effect over knockdown restricted to motor neurons. J Neurochem. 2010 Apr; 113(1):166-74.
    View in: PubMed
    Score: 0.323
  11. The effect of mutant SOD1 dismutase activity on non-cell autonomous degeneration in familial amyotrophic lateral sclerosis. Neurobiol Dis. 2009 Aug; 35(2):234-40.
    View in: PubMed
    Score: 0.308
  12. Wild-type SOD1 overexpression accelerates disease onset of a G85R SOD1 mouse. Hum Mol Genet. 2009 May 01; 18(9):1642-51.
    View in: PubMed
    Score: 0.303
  13. Truncated wild-type SOD1 and FALS-linked mutant SOD1 cause neural cell death in the chick embryo spinal cord. Neurobiol Dis. 2006 Jan; 21(1):194-205.
    View in: PubMed
    Score: 0.237
  14. Translation of dipeptide repeat proteins in C9ORF72 ALS/FTD through unique and redundant AUG initiation codons. Elife. 2023 09 07; 12.
    View in: PubMed
    Score: 0.207
  15. A rare Cu/Zn superoxide dismutase mutation causing familial amyotrophic lateral sclerosis with variable age of onset, incomplete penetrance and a sensory neuropathy. Amyotroph Lateral Scler Other Motor Neuron Disord. 2003 Sep; 4(3):162-6.
    View in: PubMed
    Score: 0.207
  16. Glutamate carboxypeptidase II inhibition protects motor neurons from death in familial amyotrophic lateral sclerosis models. Proc Natl Acad Sci U S A. 2003 Aug 05; 100(16):9554-9.
    View in: PubMed
    Score: 0.206
  17. No correlation between aggregates of Cu/Zn superoxide dismutase and cell death in familial amyotrophic lateral sclerosis. J Neurochem. 2002 Sep; 82(5):1229-38.
    View in: PubMed
    Score: 0.193
  18. A C. elegans model of C9orf72-associated ALS/FTD uncovers a conserved role for eIF2D in RAN translation. Nat Commun. 2021 10 15; 12(1):6025.
    View in: PubMed
    Score: 0.182
  19. The role of immunophilins in mutant superoxide dismutase-1linked familial amyotrophic lateral sclerosis. Proc Natl Acad Sci U S A. 1999 Mar 16; 96(6):3251-6.
    View in: PubMed
    Score: 0.152
  20. Poloxamer 188 decreases membrane toxicity of mutant SOD1 and ameliorates pathology observed in SOD1 mouse model for ALS. Neurobiol Dis. 2018 07; 115:115-126.
    View in: PubMed
    Score: 0.142
  21. Mutant superoxide dismutase-1-linked familial amyotrophic lateral sclerosis: molecular mechanisms of neuronal death and protection. J Neurosci. 1997 Nov 15; 17(22):8756-66.
    View in: PubMed
    Score: 0.139
  22. TIA1 Mutations in Amyotrophic Lateral Sclerosis and Frontotemporal Dementia Promote Phase Separation and Alter Stress Granule Dynamics. Neuron. 2017 Aug 16; 95(4):808-816.e9.
    View in: PubMed
    Score: 0.136
  23. Evidence for an early innate immune response in the motor cortex of ALS. J Neuroinflammation. 2017 06 26; 14(1):129.
    View in: PubMed
    Score: 0.135
  24. Apical dendrite degeneration, a novel cellular pathology for Betz cells in ALS. Sci Rep. 2017 02 06; 7:41765.
    View in: PubMed
    Score: 0.131
  25. S-acylation of SOD1, CCS, and a stable SOD1-CCS heterodimer in human spinal cords from ALS and non-ALS subjects. Sci Rep. 2017 01 25; 7:41141.
    View in: PubMed
    Score: 0.131
  26. Gastrostomy tube placement is safe in advanced amyotrophic lateral sclerosis. Neurol Res. 2017 Jan; 39(1):16-22.
    View in: PubMed
    Score: 0.130
  27. Amyotrophic lateral sclerosis and viruses. Clin Neurosci. 1995-1996; 3(6):360-7.
    View in: PubMed
    Score: 0.114
  28. Coexistence of amyotrophic lateral sclerosis and Werdnig-Hoffmann disease within a family. Muscle Nerve. 1993 Dec; 16(12):1416.
    View in: PubMed
    Score: 0.105
  29. Neuromuscular transmission in amyotrophic lateral sclerosis. Muscle Nerve. 1993 Nov; 16(11):1193-203.
    View in: PubMed
    Score: 0.105
  30. Amyotrophic lateral sclerosis and structural defects in Cu,Zn superoxide dismutase. Science. 1993 Aug 20; 261(5124):1047-51.
    View in: PubMed
    Score: 0.103
  31. Palmitoylation of superoxide dismutase 1 (SOD1) is increased for familial amyotrophic lateral sclerosis-linked SOD1 mutants. J Biol Chem. 2013 Jul 26; 288(30):21606-17.
    View in: PubMed
    Score: 0.102
  32. Mutant SOD1 forms ion channel: implications for ALS pathophysiology. Neurobiol Dis. 2012 Mar; 45(3):831-8.
    View in: PubMed
    Score: 0.090
  33. Astrocyte loss of mutant SOD1 delays ALS disease onset and progression in G85R transgenic mice. Hum Mol Genet. 2011 Jan 15; 20(2):286-93.
    View in: PubMed
    Score: 0.085
  34. Polyclonal IgM anti-GM1 ganglioside antibody in patients with motor neuron disease and variants. Ann Neurol. 1990 May; 27(5):558-63.
    View in: PubMed
    Score: 0.082
  35. Failure to detect enterovirus in the spinal cord of ALS patients using a sensitive RT-PCR method. Neurology. 2004 Apr 27; 62(8):1372-7.
    View in: PubMed
    Score: 0.054
  36. Nucleic acid probes in the study of amyotrophic lateral sclerosis. Adv Neurol. 1982; 36:317-29.
    View in: PubMed
    Score: 0.046
  37. Amyotrophic lateral sclerosis with antecedent poliomyelitis. Arch Neurol. 1980 May; 37(5):312-3.
    View in: PubMed
    Score: 0.041
  38. Failure to detect poliovirus genetic information in amyotrophic lateral sclerosis. Ann Neurol. 1979 Apr; 5(4):402-3.
    View in: PubMed
    Score: 0.038
  39. Intermuscular coherence in amyotrophic lateral sclerosis: A preliminary assessment. Muscle Nerve. 2017 06; 55(6):862-868.
    View in: PubMed
    Score: 0.033
  40. Patients with amyotrophic lateral sclerosis receiving long-term mechanical ventilation. Advance care planning and outcomes. Chest. 1996 Jul; 110(1):249-55.
    View in: PubMed
    Score: 0.032
  41. Home ventilation for amyotrophic lateral sclerosis patients: outcomes, costs, and patient, family, and physician attitudes. Neurology. 1993 Feb; 43(2):438-43.
    View in: PubMed
    Score: 0.025
  42. Amyotrophic lateral sclerosis and life-sustaining therapy: patients' desires for information, participation in decision making, and life-sustaining therapy. Mayo Clin Proc. 1991 Sep; 66(9):906-13.
    View in: PubMed
    Score: 0.023
  43. Linkage analysis in familial amyotrophic lateral sclerosis. Neurology. 1989 Jul; 39(7):919-25.
    View in: PubMed
    Score: 0.019
  44. Intrafamilial heterogeneity in hereditary motor neuron disease. Neurology. 1992 Aug; 42(8):1488-92.
    View in: PubMed
    Score: 0.006
  45. Circulating immune complexes in neurologic disease. Neurology. 1981 Nov; 31(11):1402-7.
    View in: PubMed
    Score: 0.003
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Publication scores are based on many factors, including how long ago they were written and whether the person is a first or senior author.