Raymond P. Roos to Mutation
This is a "connection" page, showing publications Raymond P. Roos has written about Mutation.
Connection Strength
1.157
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Mutant SOD1 knockdown in all cell types ameliorates disease in G85R SOD1 mice with a limited additional effect over knockdown restricted to motor neurons. J Neurochem. 2010 Apr; 113(1):166-74.
Score: 0.165
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Restricted expression of mutant SOD1 in spinal motor neurons and interneurons induces motor neuron pathology. Neurobiol Dis. 2008 Mar; 29(3):400-8.
Score: 0.141
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A rare Cu/Zn superoxide dismutase mutation causing familial amyotrophic lateral sclerosis with variable age of onset, incomplete penetrance and a sensory neuropathy. Amyotroph Lateral Scler Other Motor Neuron Disord. 2003 Sep; 4(3):162-6.
Score: 0.106
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Mutant presenilin-1 induces apoptosis and downregulates Akt/PKB. J Neurosci. 1999 Jul 01; 19(13):5360-9.
Score: 0.079
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Processing of wild-type and mutant familial Alzheimer's disease-associated presenilin-1 in cultured neurons. J Neurochem. 1999 Jul; 73(1):31-40.
Score: 0.079
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Poloxamer 188 decreases membrane toxicity of mutant SOD1 and ameliorates pathology observed in SOD1 mouse model for ALS. Neurobiol Dis. 2018 07; 115:115-126.
Score: 0.073
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TIA1 Mutations in Amyotrophic Lateral Sclerosis and Frontotemporal Dementia Promote Phase Separation and Alter Stress Granule Dynamics. Neuron. 2017 Aug 16; 95(4):808-816.e9.
Score: 0.070
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Palmitoylation of superoxide dismutase 1 (SOD1) is increased for familial amyotrophic lateral sclerosis-linked SOD1 mutants. J Biol Chem. 2013 Jul 26; 288(30):21606-17.
Score: 0.052
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Mutant SOD1 forms ion channel: implications for ALS pathophysiology. Neurobiol Dis. 2012 Mar; 45(3):831-8.
Score: 0.046
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Astrocyte loss of mutant SOD1 delays ALS disease onset and progression in G85R transgenic mice. Hum Mol Genet. 2011 Jan 15; 20(2):286-93.
Score: 0.043
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Truncated wild-type SOD1 and FALS-linked mutant SOD1 cause neural cell death in the chick embryo spinal cord. Neurobiol Dis. 2006 Jan; 21(1):194-205.
Score: 0.030
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Molecular mechanisms of attenuation of the Sabin strain of poliovirus type 3. J Virol. 2004 Oct; 78(20):11097-107.
Score: 0.029
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No correlation between aggregates of Cu/Zn superoxide dismutase and cell death in familial amyotrophic lateral sclerosis. J Neurochem. 2002 Sep; 82(5):1229-38.
Score: 0.025
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Cell-specific proteins regulate viral RNA translation and virus-induced disease. EMBO J. 2001 Dec 03; 20(23):6899-908.
Score: 0.023
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Novel mutations in spastin gene and absence of correlation with age at onset of symptoms. Neurology. 2000 Nov 14; 55(9):1388-90.
Score: 0.022
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What happens when mutant neuroserpins get into bad shape. Lancet. 2000 Feb 19; 355(9204):590-1.
Score: 0.021
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The prion diseases. Semin Neurol. 2000; 20(3):337-52.
Score: 0.021
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The role of beta-catenin stability in mutant PS1-associated apoptosis. Neuroreport. 1999 Aug 20; 10(12):2527-32.
Score: 0.020
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The role of immunophilins in mutant superoxide dismutase-1linked familial amyotrophic lateral sclerosis. Proc Natl Acad Sci U S A. 1999 Mar 16; 96(6):3251-6.
Score: 0.019
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A protein critical for a Theiler's virus-induced immune system-mediated demyelinating disease has a cell type-specific antiapoptotic effect and a key role in virus persistence. J Virol. 1998 Nov; 72(11):8605-12.
Score: 0.019
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S-acylation of SOD1, CCS, and a stable SOD1-CCS heterodimer in human spinal cords from ALS and non-ALS subjects. Sci Rep. 2017 01 25; 7:41141.
Score: 0.017
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The effect of Theiler's murine encephalomyelitis virus (TMEV) VP1 carboxyl region on the virus-induced central nervous system disease. J Neurovirol. 1995 Mar; 1(1):101-10.
Score: 0.015
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Amyotrophic lateral sclerosis and structural defects in Cu,Zn superoxide dismutase. Science. 1993 Aug 20; 261(5124):1047-51.
Score: 0.013
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Theiler's murine encephalomyelitis virus neutralization escape mutants have a change in disease phenotype. J Virol. 1989 Oct; 63(10):4469-73.
Score: 0.010
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Trypsin-sensitive neutralization site on VP1 of Theiler's murine encephalomyelitis viruses. J Virol. 1988 Sep; 62(9):3527-9.
Score: 0.009
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Analysis of Theiler's virus isolates from persistently infected mouse nervous tissue. J Gen Virol. 1983 Mar; 64 Pt 3:701-6.
Score: 0.006
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L* protein of the DA strain of Theiler's murine encephalomyelitis virus is important for virus growth in a murine macrophage-like cell line. J Virol. 1998 Jun; 72(6):4950-5.
Score: 0.005