James A. Mastrianni to Prions
This is a "connection" page, showing publications James A. Mastrianni has written about Prions.
Connection Strength
3.221
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Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease. J Neurosci. 2012 Sep 05; 32(36):12396-405.
Score: 0.430
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The prion diseases. J Geriatr Psychiatry Neurol. 2010 Dec; 23(4):277-98.
Score: 0.377
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A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. J Neurosci. 2009 Aug 12; 29(32):10072-80.
Score: 0.348
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Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation. J Virol. 2007 Mar; 81(6):2831-7.
Score: 0.289
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Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia. Ann Neurol. 2005 Dec; 58(6):858-64.
Score: 0.269
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The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation. J Biol Chem. 2005 Jul 22; 280(29):27236-43.
Score: 0.260
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Wrinkles and folds of the prion protein. Neurology. 2003 Nov 11; 61(9):1168-9.
Score: 0.233
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Anle138b prevents PrP plaque accumulation in Tg(PrP-A116V) mice but does not mitigate clinical disease. J Gen Virol. 2019 06; 100(6):1027-1037.
Score: 0.171
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Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease. Neurology. 1996 Nov; 47(5):1305-12.
Score: 0.143
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Familial prion disease with Alzheimer disease-like tau pathology and clinical phenotype. Ann Neurol. 2011 Apr; 69(4):712-20.
Score: 0.097
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Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Ann Neurol. 2010 Aug; 68(2):162-72.
Score: 0.093
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A novel human disease with abnormal prion protein sensitive to protease. Ann Neurol. 2008 Jun; 63(6):697-708.
Score: 0.080
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The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPSc. J Virol. 2006 Sep; 80(17):8521-9.
Score: 0.071
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Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A. 2003 Apr 15; 100(8):4784-9.
Score: 0.056
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Inherited prion disease caused by the V210I mutation: transmission to transgenic mice. Neurology. 2001 Dec 26; 57(12):2198-205.
Score: 0.051
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The prion diseases. Semin Neurol. 2000; 20(3):337-52.
Score: 0.045
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Prion protein conformation in a patient with sporadic fatal insomnia. N Engl J Med. 1999 May 27; 340(21):1630-8.
Score: 0.043
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A transmembrane form of the prion protein in neurodegenerative disease. Science. 1998 Feb 06; 279(5352):827-34.
Score: 0.039
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The prion diseases: Creutzfeldt-Jakob, Gerstmann-Sträussler-Scheinker, and related disorders. J Geriatr Psychiatry Neurol. 1998; 11(2):78-97.
Score: 0.039
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Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein. Cell. 1995 Oct 06; 83(1):79-90.
Score: 0.033
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Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene. Mol Med. 1995 Sep; 1(6):607-13.
Score: 0.033
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Identifying key components of the PrPC-PrPSc replicative interface. J Biol Chem. 2008 Dec 05; 283(49):34021-8.
Score: 0.020