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One or more keywords matched the following items that are connected to Mastrianni, James A.
Item TypeName
Concept Prions
Academic Article Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene.
Academic Article Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease.
Academic Article Prion protein conformation in a patient with sporadic fatal insomnia.
Academic Article The prion diseases: Creutzfeldt-Jakob, Gerstmann-Sträussler-Scheinker, and related disorders.
Academic Article A transmembrane form of the prion protein in neurodegenerative disease.
Academic Article The prion diseases.
Academic Article Inherited prion disease caused by the V210I mutation: transmission to transgenic mice.
Academic Article Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene.
Academic Article The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPSc.
Academic Article The AGAAAAGA palindrome in PrP is required to generate a productive PrPSc-PrPC complex that leads to prion propagation.
Academic Article A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP.
Academic Article Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia.
Academic Article Familial prion disease with Alzheimer disease-like tau pathology and clinical phenotype.
Academic Article Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein.
Academic Article The prion diseases.
Academic Article Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein.
Academic Article Identifying key components of the PrPC-PrPSc replicative interface.
Academic Article Rapamycin delays disease onset and prevents PrP plaque deposition in a mouse model of Gerstmann-Sträussler-Scheinker disease.
Academic Article Wrinkles and folds of the prion protein.
Academic Article Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation.
Academic Article A novel human disease with abnormal prion protein sensitive to protease.
Academic Article Generation of a new form of human PrP(Sc) in vitro by interspecies transmission from cervid prions.
Academic Article Impaired transmissibility of atypical prions from genetic CJDG114V.
Academic Article Anle138b prevents PrP plaque accumulation in Tg(PrP-A116V) mice but does not mitigate clinical disease.
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