Diffuse Cerebral Sclerosis of Schilder
"Diffuse Cerebral Sclerosis of Schilder" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A rare central nervous system demyelinating condition affecting children and young adults. Pathologic findings include a large, sharply defined, asymmetric focus of myelin destruction that may involve an entire lobe or cerebral hemisphere. The clinical course tends to be progressive and includes dementia, cortical blindness, cortical deafness, spastic hemiplegia, and pseudobulbar palsy. Concentric sclerosis of Balo is differentiated from diffuse cerebral sclerosis of Schilder by the pathologic finding of alternating bands of destruction and preservation of myelin in concentric rings. Alpers' Syndrome refers to a heterogeneous group of diseases that feature progressive cerebral deterioration and liver disease. (From Adams et al., Principles of Neurology, 6th ed, p914; Dev Neurosci 1991;13(4-5):267-73)
Descriptor ID |
D002549
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MeSH Number(s) |
C10.114.375.112 C10.228.140.400 C10.228.140.695.562.112 C10.228.518.562.112 C10.314.350.112 C20.111.258.250.175
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Concept/Terms |
Diffuse Cerebral Sclerosis of Schilder- Diffuse Cerebral Sclerosis of Schilder
- Myelinoclastic Diffuse Sclerosis
- Diffuse Scleroses, Myelinoclastic
- Diffuse Sclerosis, Myelinoclastic
- Myelinoclastic Diffuse Scleroses
- Scleroses, Myelinoclastic Diffuse
- Sclerosis, Myelinoclastic Diffuse
- Poliodystrophia Cerebri
- Schilder Disease
- Disease, Schilder
- Encephalitis Periaxialis Concentrica
- Cerebral Sclerosis, Diffuse
- Diffuse Cerebral Scleroses
- Diffuse Cerebral Sclerosis
- Sclerosis, Diffuse Cerebral
- Encephalitis Periaxialis
- Encephalitis Periaxialis Diffusa
- Schilder's Disease
- Disease, Schilder's
- Schilders Disease
Balo Concentric Sclerosis- Balo Concentric Sclerosis
- Concentric Sclerosis, Balo
- Balo's Concentric Sclerosis
- Concentric Sclerosis, Balo's
- Scleroses, Balo's Concentric
Alpers Syndrome- Alpers Syndrome
- Syndrome, Alpers
- Progressive Sclerosing Poliodystrophy
- Progressive Sclerosing Poliodystrophies
- Alpers-Huttenlocher Syndrome
- Alpers Huttenlocher Syndrome
- Syndrome, Alpers-Huttenlocher
- Alpers Progressive Infantile Poliodystrophy
- Alpers' Disease
- Alper Disease
- Alper's Disease
- Disease, Alpers'
- Alpers' Syndrome
- Alper Syndrome
- Alper's Syndrome
- Progressive Neuronal Degeneration of Childhood with Liver Disease
- Alpers Diffuse Degeneration of Cerebral Gray Matter with Hepatic Cirrhosis
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Below are MeSH descriptors whose meaning is more general than "Diffuse Cerebral Sclerosis of Schilder".
Below are MeSH descriptors whose meaning is more specific than "Diffuse Cerebral Sclerosis of Schilder".
This graph shows the total number of publications written about "Diffuse Cerebral Sclerosis of Schilder" by people in this website by year, and whether "Diffuse Cerebral Sclerosis of Schilder" was a major or minor topic of these publications.
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Year | Major Topic | Minor Topic | Total |
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1986 | 1 | 0 | 1 | 1987 | 1 | 0 | 1 | 1997 | 1 | 0 | 1 |
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Below are the most recent publications written about "Diffuse Cerebral Sclerosis of Schilder" by people in Profiles.
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Schwabe MJ, Dobyns WB, Burke B, Armstrong DL. Valproate-induced liver failure in one of two siblings with Alpers disease. Pediatr Neurol. 1997 May; 16(4):337-43.
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Hong-Magno ET, Muraki AS, Huttenlocher PR. Atypical CT scans in adrenoleukodystrophy. J Comput Assist Tomogr. 1987 Mar-Apr; 11(2):333-6.
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Kelley RI, Datta NS, Dobyns WB, Hajra AK, Moser AB, Noetzel MJ, Zackai EH, Moser HW. Neonatal adrenoleukodystrophy: new cases, biochemical studies, and differentiation from Zellweger and related peroxisomal polydystrophy syndromes. Am J Med Genet. 1986 Apr; 23(4):869-901.
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Huckman MS, Fox JH, Ramsey RG. Computed tomography in the diagnosis of degenerative diseases of the brain. Semin Roentgenol. 1977 Jan; 12(1):63-75.
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Duda EE, Huttenlocher PR. Computed tomography in adrenoleukodystrophy. Correlation of radiological and histological findings. Radiology. 1976 Aug; 120(2):349-50.
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