Creutzfeldt-Jakob Syndrome
"Creutzfeldt-Jakob Syndrome" is a descriptor in the National Library of Medicine's controlled vocabulary thesaurus,
MeSH (Medical Subject Headings). Descriptors are arranged in a hierarchical structure,
which enables searching at various levels of specificity.
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
Descriptor ID |
D007562
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MeSH Number(s) |
C10.228.140.380.165 C10.228.228.800.230 F03.087.400.300
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Concept/Terms |
Creutzfeldt-Jakob Syndrome- Creutzfeldt-Jakob Syndrome
- Creutzfeldt Jakob Syndrome
- Syndrome, Creutzfeldt-Jakob
- Creutzfeldt Jacob Disease
- Disease, Creutzfeldt Jacob
- Jacob Disease, Creutzfeldt
- Spongiform Encephalopathy, Subacute
- Encephalopathies, Subacute Spongiform
- Encephalopathy, Subacute Spongiform
- Spongiform Encephalopathies, Subacute
- Subacute Spongiform Encephalopathies
- Subacute Spongiform Encephalopathy
- Jakob-Creutzfeldt Disease
- Disease, Jakob-Creutzfeldt
- Jakob Creutzfeldt Disease
- Jakob-Creutzfeldt Syndrome
- Jakob Creutzfeldt Syndrome
- Syndrome, Jakob-Creutzfeldt
- CJD (Creutzfeldt-Jakob Disease)
- CJD (Creutzfeldt Jakob Disease)
- Creutzfeldt-Jakob Disease
- Creutzfeldt Jakob Disease
- Disease, Creutzfeldt-Jakob
Creutzfeldt-Jakob Disease, Familial- Creutzfeldt-Jakob Disease, Familial
- Creutzfeldt Jakob Disease, Familial
- Creutzfeldt-Jakob Diseases, Familial
- Disease, Familial Creutzfeldt-Jakob
- Familial Creutzfeldt-Jakob Diseases
- Familial Creutzfeldt-Jakob Disease
- Familial Creutzfeldt Jakob Disease
New Variant Creutzfeldt-Jakob Disease- New Variant Creutzfeldt-Jakob Disease
- New Variant Creutzfeldt Jakob Disease
- V-CJD (Variant-Creutzfeldt-Jakob Disease)
- Variant Creutzfeldt-Jakob Disease
- Creutzfeldt-Jakob Disease, Variant
- Variant Creutzfeldt Jakob Disease
- Creutzfeldt-Jakob Disease, New Variant
- Creutzfeldt Jakob Disease, New Variant
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Below are MeSH descriptors whose meaning is more general than "Creutzfeldt-Jakob Syndrome".
Below are MeSH descriptors whose meaning is more specific than "Creutzfeldt-Jakob Syndrome".
This graph shows the total number of publications written about "Creutzfeldt-Jakob Syndrome" by people in this website by year, and whether "Creutzfeldt-Jakob Syndrome" was a major or minor topic of these publications.
To see the data from this visualization as text, click here.
Year | Major Topic | Minor Topic | Total |
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1982 | 1 | 0 | 1 | 1985 | 0 | 1 | 1 | 1986 | 0 | 1 | 1 | 1995 | 2 | 0 | 2 | 1996 | 1 | 0 | 1 | 1997 | 2 | 0 | 2 | 1998 | 2 | 0 | 2 | 1999 | 1 | 0 | 1 | 2000 | 2 | 1 | 3 | 2001 | 1 | 0 | 1 | 2003 | 0 | 1 | 1 | 2009 | 0 | 1 | 1 | 2010 | 0 | 1 | 1 |
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Below are the most recent publications written about "Creutzfeldt-Jakob Syndrome" by people in Profiles.
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Brown K, Mastrianni JA. The prion diseases. J Geriatr Psychiatry Neurol. 2010 Dec; 23(4):277-98.
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Yang W, Cook J, Rassbach B, Lemus A, DeArmond SJ, Mastrianni JA. A New Transgenic Mouse Model of Gerstmann-Straussler-Scheinker Syndrome Caused by the A117V Mutation of PRNP. J Neurosci. 2009 Aug 12; 29(32):10072-80.
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Korth C, Kaneko K, Groth D, Heye N, Telling G, Mastrianni J, Parchi P, Gambetti P, Will R, Ironside J, Heinrich C, Tremblay P, DeArmond SJ, Prusiner SB. Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene. Proc Natl Acad Sci U S A. 2003 Apr 15; 100(8):4784-9.
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Roos RP. Controlling new prion diseases. N Engl J Med. 2001 May 17; 344(20):1548-51.
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Gibbons RV, Holman RC, Belay ED, Schonberger LB. Creutzfeldt-Jakob disease in the United States: 1979-1998. JAMA. 2000 Nov 08; 284(18):2322-3.
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Worrall BB, Rowland LP, Chin SS, Mastrianni JA. Amyotrophy in prion diseases. Arch Neurol. 2000 Jan; 57(1):33-8.
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Mastrianni JA, Roos RP. The prion diseases. Semin Neurol. 2000; 20(3):337-52.
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Weihl CC, Roos RP. Creutzfeldt-Jakob disease, new variant creutzfeldt-jakob disease, and bovine spongiform encephalopathy. Neurol Clin. 1999 Nov; 17(4):835-59.
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Patry D, Curry B, Easton D, Mastrianni JA, Hogan DB. Creutzfeldt-Jakob disease (CJD) after blood product transfusion from a donor with CJD. Neurology. 1998 Jun; 50(6):1872-3.
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Mastrianni JA. The prion diseases: Creutzfeldt-Jakob, Gerstmann-Sträussler-Scheinker, and related disorders. J Geriatr Psychiatry Neurol. 1998; 11(2):78-97.
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